abstract: Ovarian steroid cell tumor with biallelic adenomatous polyposis coli inactivation in a patient with familial adenomatous polyposis (FAP)

"Our findings provide the first evidence that ovarian steroid cell tumors may be an extracolonic manifestation of FAP (familial adenomatous polyposis - colorectal cancer syndrome) and implicate β-catenin activation as an oncogenic mechanism in ovarian steroid cell tumorigenesis."